Complex orbital angiomyoma with features of a lymphangiohemangioma

Jakobiec F, Zakka F, Yoon M. Complex orbital angiomyoma with features of a lymphangiohemangioma. Ophthalmic Plast Reconstr Surg. 2013;29(2):e61–5.

Abstract

A 31-year-old woman developed left frontal headache and retrobulbar pain with exotropia and mild limitation of upgaze without proptosis. Imaging studies disclosed a circumscribed mass measuring 1.5 cm in the greatest diameter. At surgery, the lesion was adherent to the surrounding normal orbital tissues, making for a difficult and dangerous resection. Histopathologically and immunohistochemically, the lesion was a mixed cavernous angiomatous (CD31-positive) and lymphangiomatous (D2-40-positive) tumor with abundant interstitial smooth muscle. Such lesions can present significant surgical challenges due to incomplete pseudoencapsulation.
Last updated on 03/06/2023